Grant Detail
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Frontotemporal degeneration: a basis for clinical trials
30 September 2003 - 31 August 2007
NATIONAL INSTITUTE ON AGING
Total Funding: $ 1,649,076
In order to test drugs in patients with tauopathies, knowledge of the natural history of the frontotemporal lobar dementias (FTLD) must be expressed in terms suitable for designing clinical trials. Without valid estimates of change over 6 or 12 months, instruments appropriate for trials and sample sizes for the trials simply cannot be determined. We are proposing a 4 year, multi-site, longitudinal study of patients with FTLD in which we will recruit subjects using standardized criteria. The specific aims of this project are 1) determine the ratio between change and variance in cognitive, behavioral and functional instruments in order to estimate power to detect treatment effects with each instrument in future clinical trials; 2) perform serial MR imaging to determine the magnitude of change and its variance in global and regional frontal or temporal brain volume in order to estimate power to detect treatment effects on brain volume in future clinical trials; 3) develop a composite FTLD-subtype-specific cognitive instrument for use in clinical trials; and 4) determine whether ApoE genotype and tau haplotype are associated with rate of progression on cognitive, behavioral, functional or imaging in FTLD. We propose to involve 3 Alzheimer Disease Centers (Mayo Rochester/Jacksonville, UCLA and Arizona) plus the University of California- San Francisco to recruit 120 patients with FTLD. We shall recruit patients with the behavioral-dysexecutive syndrome of fronto-temporal dementia, patients with semantic dementia, and patients with progressive nonfluent aphasia. Operational criteria for these 3 syndromes have been developed that will meet rigorous standards suitable for clinical trial recruitment. Subjects will be examined with cognitive, behavioral, functional assessments as well as MR imaging at baseline and 12 months. Key outcomes will include estimates of change and its variability over 1 year on MR imaging, change on cognitive tasks including the composite task, and change on functional and behavioral measures. While the study will also develop a wealth of new knowledge about the relationships between cognition, behavior and brain structure in FTLD, the essential product of this study will be the principles underlying a rationale design for trials of drugs for FTLD.
18 Resulting Publications
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1.
2013Po H Lu; Mario F Mendez; Grace J Lee; Alex D Leow; Hyun-Woo Lee; Jill Shapira; Elvira Jimenez; Bradley B Boeve; Richard J Caselli; Neill R Graff-Radford; et al.
Patterns of brain atrophy in clinical variants of frontotemporal lobar degeneration.
Dementia and geriatric cognitive disorders 2013;35(1-2):34-50. -
2.
2011David S Knopman; Sandra Weintraub; Vernon S Pankratz
Language and behavior domains enhance the value of the clinical dementia rating scale.
Alzheimer's & dementia : the journal of the Alzheimer's Association 2011;7(3):293-9. -
3.
2010J L Whitwell; C R Jack; B F Boeve; J E Parisi; J E Ahlskog; D A Drubach; M L Senjem; D S Knopman; R C Petersen; D W Dickson; et al.
Imaging correlates of pathology in corticobasal syndrome.
Neurology 2010;75(21):1879-87. -
4.
2010Serguei V S Pakhomov; Glenn E Smith; Dustin Chacon; Yara Feliciano; Neill Graff-Radford; Richard Caselli; David S Knopman
Cognitive and behavioral neurology : official journal of the Society for Behavioral and Cognitive Neurology 2010;23(3):165-77. -
5.
2010K Kantarci; B F Boeve; Z K Wszolek; R Rademakers; J L Whitwell; M C Baker; M L Senjem; A R Samikoglu; D S Knopman; R C Petersen; et al.
MRS in presymptomatic MAPT mutation carriers: a potential biomarker for tau-mediated pathology.
Neurology 2010;75(9):771-8. -
6.
2010P Vemuri; H J Wiste; S D Weigand; D S Knopman; J Q Trojanowski; L M Shaw; M A Bernstein; P S Aisen; M Weiner; R C Petersen; et al.
Serial MRI and CSF biomarkers in normal aging, MCI, and AD.
Neurology 2010;75(2):143-51. -
7.
2010J L Whitwell; R Avula; M L Senjem; K Kantarci; S D Weigand; A Samikoglu; H A Edmonson; P Vemuri; D S Knopman; B F Boeve; et al.
Gray and white matter water diffusion in the syndromic variants of frontotemporal dementia.
Neurology 2010;74(16):1279-87. -
8.
2010Bei Hu; Leslie Ross; John Neuhaus; David Knopman; Joel Kramer; Bradley Boeve; Richard J Caselli; Neill Graff-Radford; Mario F Mendez; Bruce L Miller; et al.
Off-label medication use in frontotemporal dementia.
American journal of Alzheimer's disease and other dementias 2010;25(2):128-33. -
9.
2010Jennifer Molano; Bradley Boeve; Tanis Ferman; Glenn Smith; Joseph Parisi; Dennis Dickson; David Knopman; Neill Graff-Radford; Yonas Geda; John Lucas; et al.
Brain : a journal of neurology 2010;133(Pt 2):540-56. -
10.
2009K A Josephs; J L Whitwell; D S Knopman; B F Boeve; P Vemuri; M L Senjem; J E Parisi; R J Ivnik; D W Dickson; R C Petersen; et al.
Two distinct subtypes of right temporal variant frontotemporal dementia.
Neurology 2009;73(18):1443-50. -
11.
2009S R Lesage; T H Mosley; T Y Wong; M Szklo; D Knopman; D J Catellier; S R Cole; R Klein; J Coresh; L H Coker; et al.
Retinal microvascular abnormalities and cognitive decline: the ARIC 14-year follow-up study.
Neurology 2009;73(11):862-8. -
12.
2009D S Knopman; C R Jack; J H Kramer; B F Boeve; R J Caselli; N R Graff-Radford; M F Mendez; B L Miller; N D Mercaldo
Brain and ventricular volumetric changes in frontotemporal lobar degeneration over 1 year.
Neurology 2009;72(21):1843-9. -
13.
2008David S Knopman; Joel H Kramer; Bradley F Boeve; Richard J Caselli; Neill R Graff-Radford; Mario F Mendez; Bruce L Miller; Nathaniel Mercaldo
Development of methodology for conducting clinical trials in frontotemporal lobar degeneration.
Brain : a journal of neurology 2008;131(Pt 11):2957-68. -
14.
2007B F Boeve; M H Silber; C B Saper; T J Ferman; D W Dickson; J E Parisi; E E Benarroch; J E Ahlskog; G E Smith; R C Caselli; et al.
Pathophysiology of REM sleep behaviour disorder and relevance to neurodegenerative disease.
Brain : a journal of neurology 2007;130(Pt 11):2770-88. -
15.
2007David S Knopman; Bradley S Boeve; Richard J Caselli; Neill R Graff-Radford; Joel H Kramer; Mario F Mendez; Bruce L Miller
Longitudinal tracking of FTLD: toward developing clinical trial methodology.
Alzheimer disease and associated disorders 2007;21(4):S58-63. -
16.
2006Jennifer Gass; Ashley Cannon; Ian R Mackenzie; Bradley Boeve; Matt Baker; Jennifer Adamson; Richard Crook; Stacey Melquist; Karen Kuntz; Ron Petersen; et al.
Mutations in progranulin are a major cause of ubiquitin-positive frontotemporal lobar degeneration.
Human molecular genetics 2006;15(20):2988-3001. -
17.
2006K A Josephs; R C Petersen; D S Knopman; B F Boeve; J L Whitwell; J R Duffy; J E Parisi; D W Dickson
Clinicopathologic analysis of frontotemporal and corticobasal degenerations and PSP.
Neurology 2006;66(1):41-8. -
18.
2005David S Knopman; Bradley F Boeve; Joseph E Parisi; Dennis W Dickson; Glenn E Smith; Robert J Ivnik; Keith A Josephs; Ronald C Petersen
Antemortem diagnosis of frontotemporal lobar degeneration.
Annals of neurology 2005;57(4):480-8.
Scientific Context
This section shows information that has been computed by using the fingerprint of the grant, including related publications, related experts and related grants - all with fingerprints representing significant amounts of overlap between their fingerprint and this grant. The red dots indicate whether those experts or terms actually appear within this grant, showing potential and actual connections.
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Journal of Alzheimer's disease : JAD 2006;9(3 Suppl):187-94. -
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